A12930
Size
  • 50ul
  • 100ul
Price
  • $129
  • $229
Qty
Product description

disease:Defects in MT-ATP6 are a cause of infantile bilateral striatal necrosis [MIM:500003]. Bilateral striatal necrosis is a neurological disorder resembling Leigh syndrome.,disease:Defects in MT-ATP6 are a cause of Leber hereditary optic neuropathy (LH

Source
Rabbit
Applications
WB,ELISA
Reactivity
Human
Dilution
WB 1:500-2000 ELISA 1:5000-20000
Storage
-20°C/1 year
Specificity
COX3 Polyclonal Antibody detects endogenous levels of protein.
Source/Purification
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
Immunogen
Synthesized peptide derived from human protein . at AA range: 1-80
Uniprot No
P00414
Form
Liquid in PBS containing 50% glycerol, and 0.02% sodium azide.
Clonality
Polyclonal
Background
disease:Defects in MT-ATP6 are a cause of infantile bilateral striatal necrosis [MIM:500003]. Bilateral striatal necrosis is a neurological disorder resembling Leigh syndrome.,disease:Defects in MT-ATP6 are a cause of Leber hereditary optic neuropathy (LH
Other
Gene_name: MT-CO3 COIII COXIII MTCO3 ; Protein_name: Cytochrome c oxidase subunit 3 (Cytochrome c oxidase polypeptide III); Expression: Blood,Bone fossil,Bones,Breast cancer,Distant normal tissue,Endometrial adenocarcin
Mol.Wt (Da)
28 kD
Concentration
1 mg/ml